Turkish Journal of Anaesthesiology & Reanimation

The Anaesthetic Management of Temporal Tumour Resection in a Patient with Type 1 Glutaric Aciduria


İstanbul Üniversitesi Cerrahpaşa Tıp Fakültesi, Anesteziyoloji ve Reanimasyon Anabilim Dalı, İstanbul, Türkiye

Turk J Anaesthesiol Reanim 2013; 41: 139-141
DOI: 10.5152/TJAR.2013.20
Read: 279 Downloads: 168 Published: 09 October 2019

Glutaric aciduria type 1 (GA-1) is an uncommon cerebral organic aciduria. The risk of acute encephalopathic crises and metabolic acidosis may present during anaesthetic and surgical or postsurgical periods. Few cases with GA-1 who underwent general anaesthesia have been reported previously, and there are no data on long-term anaesthetic management of patients with GA-1. We report the anaesthetic management of temporal tumour resection that lasted for 8 hours in a 16-year-old patient with GA1, and discuss the risks of malignant hyperthermia and propofol infusion syndrome.

EISSN 2667-6370