Case Report

Anaesthetic Challenges in a Rare Syndrome: Perioperative Management of a Patient with POEMS Syndrome Who Underwent Umbilical Hernioplasty

10.5152/TJAR.2019.53824

  • Sajil M. Sajan
  • Neeraja Ajayan
  • Gayatri Devi Nair
  • Karen Ruby Lionel
  • Ajay Prasad Hrishi

Received Date: 15.10.2018 Accepted Date: 27.10.2018 Turk J Anaesthesiol Reanim 2019;47(5):420-422

Polyneuropathy, organomegaly, endocrinopathy, monoclonal gammopathy, and skin changes (POEMS) syndrome also known as ‘Crow Fukase syndrome’ is a rare paraneoplastic disorder, first described by Crow and Fukase with distinctive features of polyradiculoneuropathy, organomegaly, endocrinopathy, monoclonal gammopathy and skin changes. There is a paucity of literature about anaesthetic management of patients with POEMS syndrome with isolated case reports of surgery under general anaesthesia and central neuraxial blockade. We present here the anaesthetic management of a patient with POEMS syndrome posted for umbilical hernia repair, which was successfully managed with a transverse abdominis plane (TAP) block.

Keywords: POEMS, TAP block, umbilical hernia