Turkish Journal of Anaesthesiology & Reanimation
CASE REPORT

Anesthetic Management of A Patient with Charcot-Marie-Tooth Disease for 2-stage Revision of Total Knee Replacement

1.

Department of Anesthesiology, Attikon University Hospital, National and Kapodistrian University of Athens, Athens, Greece

Turk J Anaesthesiol Reanim 2021; 49: 178-180
DOI: 10.5152/TJAR.2021.513
Read: 76 Downloads: 38 Published: 21 April 2021

Charcot-Marie-Tooth disease is characterised by hereditary motor and sensory neuropathy. Its anaesthetic management is challenging owing to the unpredictable response observed in patients, especially to non-depolarising neuromuscular blocking drugs, and the risk of malignant hyperthermia and cardiorespiratory complications. A 66-year-old woman underwent anaesthesia for 2 different surgical procedures, a 2-stage revision of total knee replacement over a 4-month period. She presented with severe anatomic disorders, accompanied by severe motor and sensory impairment. An anaesthetic plan without neuromuscular blocking drugs or volatile anaesthetics, using a clean ventilator, with dantrolene available, was successfully used both times. There were no complications during the administration of general anaesthesia or postoperatively at the post-anaesthesia care unit, and the patient did not complain of pain at any time. General anaesthesia with a careful selection of anaesthetic drugs proved to be a safe option for the management of a patient with Charcot-Marie-Tooth disease.

Cite this article as: Soulioti E, Kavezou F, Efstathiou G, Batistaki C, Karakosta A. Anesthetic Management of A Patient with Charcot-Marie-Tooth Disease for 2-stage Revision of Total Knee Replacement. Turk J Anaesthesiol Reanim 2021; 49(2): 178-80.

Files
EISSN 2667-6370